Extraskeletal Ewing's sarcoma (EES) is a type of Ewing's sarcoma that arises in soft tissue and is now regarded as a member of a family of small round cell neoplasms of bone and soft tissue, including primitive neuroectodermal tumors (PNETs). EES occurs predominantly in adolescents and young adults between the ages of 10 and 30 years. The disease follows an aggressive course with a high recurrence rate. The presence of a distant metastasis is also common. EES arises in the soft tissue of either the trunk or extremities. We recently experienced two cases of EES that occurred in the chest wall. The two patients underwent wide resection and combined radiochemotherapy. There was no evidence of disease 30 and 22 months, respectively, after surgery. Although extremely rare, EES should be considered in the differential diagnosis of chest wall tumors. We report two cases of EES with a brief review of the literature.

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• Large retroperitoneal extraskeletal Ewing’s sarcoma with renal pedicle invasion: a case report
  Shu-Yu Wu, Chun-Kai Hsu, Chung-Tai Yue, Yao-Chou Tsai
  BMC Urology.2023;[Epub]     CrossRef
• Case Report: Primary Ewing Sarcoma of the Penis
  Soumen Das, Siddhartha Shankar Mishra, Kamalesh Rakshit, Rahul Agarwal
  Indian Journal of Surgical Oncology.2023; 14(3): 752.     CrossRef
• Retroperitoneal blue cell round tumor (Ewing sarcoma in a 35 years old male)- case report
  Fatema Nabeel Nedham, Veena Nagaraj, Abdulla Darwish, Thamer Abduljabbar Al-Abbasi
  International Journal of Surgery Case Reports.2022; 94: 107045.     CrossRef
• Abdominal Wall Extraskeletal Ewing's Sarcoma in an 8-Year-Old Child
  Gowri Shankar, Vinay Kumar Konamme
  Journal of Indian Association of Pediatric Surgeons.2022; 27(6): 771.     CrossRef
• Ewing Sarcoma Family Tumors: Past, Present and Future Prospects
  Adil Abbas, Mohammed N.S. Alaa
  Current Cancer Therapy Reviews.2021; 17(2): 107.     CrossRef
• Extraskeletal Ewing’s sarcoma/primitive neuroectodermal tumor of the mediastinum: Significant response to chemoradiotherapy
  MIN LIU, BAILONG LIU, LIHUA DONG, TAO HAN, LEI ZHANG
  Oncology Letters.2015; 9(2): 626.     CrossRef
• Retroperitoneal Extraskeletal Ewing's Sarcoma
  Si Hyung Lee, Byung Ik Jang
  The Korean Journal of Gastroenterology.2013; 62(4): 253.     CrossRef
• Scapular bone destruction: do not forget to think of tuberculosis in endemic areas
  Barun Kumar Sharma, Varun Kumar Singh, Kumar Nishant, Deepak Das
  BMJ Case Reports.2013; : bcr2013200051.     CrossRef
• Primary Ewing’s Sarcoma of Penis – A Rare Case Report
  Prashant Sharma, Hemang Bakshi, Yogen Chheda, Surender Beniwal
  Indian Journal of Surgical Oncology.2011; 2(4): 332.     CrossRef
• High Efficacy of Preoperative Low-Dose Radiotherapy with Sanazole (AK-2123) for Extraskeletal Ewing's Sarcoma: A Case Report
  Tomoya Sakabe, Hiroaki Murata, Eiichi Konishi, Kazutaka Koto, Naoyuki Horie, Takaaki Matsui, Yasushi Sawai, Hideya Yamazaki, Tsutomu V. Kagiya, Toshikazu Kubo
  Sarcoma.2011; 2011: 1.     CrossRef
• A Case of Cervical Ewing Sarcoma with Pulmonary Metastasis
  Jong Chul Hong, Jae Hoon Lee, Seo Hee Rha, Heon Soo Park
  Korean Journal of Otorhinolaryngology-Head and Neck Surgery.2010; 53(7): 441.     CrossRef